Anti-ETFA Rabbit Polyclonal Antibody (Alexa Fluor® 680)

BOSSBS-0494R-A680

Anti-ETFA Rabbit Polyclonal Antibody (Alexa Fluor® 680)

BOSSBS-0494R-A680

Antibody type:
Primary
Antigen name:
ETFA
Clonality:
Polyclonal
Conjugation:
Alexa Fluor® 680
Host:
Rabbit
ImmunoChemistry:
Yes
ImmunoFluorescence:
Yes
Isotype:
IgG
Reactivity:
Xenopus laevis,
Mouse
Environmentally Preferable:
Epitope:
184-260/333
Form:
Liquid
Gene ID:
2108
Antigen synonyms:
Electron transfer flavoprotein alpha subunit|ETFA_HUMAN|Electron transfer flavoprotein subunit alpha, mitochondrial|Electron transferring flavoprotein alpha polypeptide|Alpha ETF|mitochondrial|EMA|Electron transfer flavoprotein subunit alpha mitochondrial|Alpha-ETF|Electron transfer flavoprotein alpha polypeptide|electron-transfer-flavoprotein, alpha polypeptide|ETFA|Electron transfer flavoprotein subunit alpha|GA2.|ETF-alpha
Modification:
Unmodified
Storage buffer:
Aqueous buffered solution containing 0,01 M TBS (pH 7,4) with 1% BSA, 0,03% Proclin300 and 50% Glycerol
Molecular weight:
37 kDa
Storage temperature:
Store at –20 °C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
Concentration:
1 µg/µl
Shipping temperature:
4 °C
Immunogen:
KLH conjugated synthetic peptide derived from human ETFA
Tested applications:
ICC
Purification:
Purified by Protein A
Pack type:
Vial
Pk:
100 µl

ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene.

Type: Primary
Antigen: ETFA
Clonality: Polyclonal
Clone:
Conjugation: ALEXA FLUOR® 680
Public Immunogen Range: 184-260/333
Host: Rabbit
Isotype: IgG
Reactivity: Mouse, Xenopus laevis