Specifications
- Antigen name:Hydroxyacyl-CoA Dehydrogenase
- Antigen symbol:HADH
- Clonality:Polyclonal
- Conjugation:Unconjugated
- Host:Chicken
- Isotype:
- Reactivity:Human,Rat,Mouse
- Western blot:Yes
- Environmentally Preferable:
- Form:Liquid
- Antigen synonyms:HADH1|HAD|HADH|HADHSC|M/SCHAD|short chain|SCHAD|MGC8392|HHF4|hydroxyacyl-Coenzyme A dehydrogenase|L-3-hydroxyacyl-Coenzyme A dehydrogenase
- Concentration:1 mg/mL
- Immunogen:57-314
- Tested applications:Immunoaffinity Purified
- Size:50 µg
- Pk:50 µG
Specifications
About this item
FUNCTION: Plays an essential role in the mitochondrial beta-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.DISEASE: Defects in HADHSC are the cause of 3-beta-hydroxyacyl-CoA dehydrogenase deficiency (HAD deficiency) [MIM:609609]. HAD deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.
Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial antibody can be used for the detection of Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial by Western Blot.
Phosphate-Buffered Saline. No preservatives added.
Phosphate-Buffered Saline. No preservatives added.
Aliquot and store at -20°C or below. Avoid multiple freeze-thaw cycles.
Type:
Antigen: HADH
Clonality: Polyclonal
Clone:
Conjugation: Unconjugated
Epitope:
Host: Chicken
Isotype:
Reactivity: Human, Mouse, Rat